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(S)-3,4-Dihydroxybutyric acid lithium hydrate
本产品不向个人销售,仅用作科学研究,不用于任何人体实验及非科研性质的动物实验。
(S)-3,4-Dihydroxybutyric acid lithium hydrate图片
规格:98%
分子量:144.05
包装与价格:
包装价格(元)
5mg电议
10mg电议
25mg电议

产品介绍
(S)-3,4-Dihydroxybutyric acid (lithium hydrate) 是一种正常的人体尿液代谢物,在琥珀酸半醛脱氢酶 (SSADH) 缺乏症患者中浓度增加。
货号:ajcx37684
CAS:N/A
分子式:C4H9LiO5
分子量:144.05
溶解度:H2O : 125 mg/mL (867.75 mM; Need ultrasonic)
纯度:98%
存储:Store at -20°C
库存:现货

Background:

(S)-3,4-Dihydroxybutyric acid (lithium hydrate) is a normal human urinary metabolite that is excreted in increased concentration in patients with succinic semialdehyde dehydrogenase (SSADH) deficiency[1].

[1]. Shinka T, et al. Rapid and sensitive detection of urinary 4-hydroxybutyric acid and its related compounds by gas chromatography-mass spectrometry in a patient with succinic semialdehyde dehydrogenase deficiency. J Chromatogr B Analyt Technol Biomed Life Sci. 2002 Aug 25;776(1):57-63.